Substance
ID:389098
Names and Identifiers
IUPAC Traditional name
(3-methylbutanamido)acetic acid
IUPAC name
2-(3-methylbutanamido)acetic acid
Synonyms
N-IsovalerylglycineIsovalerylglycineN-IsovaleroylglycineN-(3-Methyl-1-oxobutyl)glycineN-Iso Valerylglycine
Registration numbers
CAS Number
Properties
Safety Information
MSDS Link
Product Information
Certificate of Analysis
Molecule Details
N-Isovalerylglycine is a useful diagnostic tool in the diagnosis of many organic acidemias and mitochondrial fatty acid β-oxidation defects. N-Isovalerylglycine is found in the urine of patients with isovaleric acidemia, an inborn error of leucine metabol
Molecular Spectra
No Data Available
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References
• Bonafe, L. et al.: Mol. Gen. Metab., 69, 311 (1967)
• Tanaka, K. et al.: J. Biol. Chem., 242, 2966 (1967)